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Case Reports
. 2018 Apr 4:2018:5190271.
doi: 10.1155/2018/5190271. eCollection 2018.

Primary Pleuropulmonary Synovial Sarcoma: A Case

Fatima Zahra Mrabet  1   2 , Hafsa El Ouazzani  2   3 , Leila El Akkari  1   2 , Sanaa Hammi  1   2 , Jamal Eddine Bourkadi  1   2 , Fouad Zouaidia  2   3
Affiliations
Case Reports

Primary Pleuropulmonary Synovial Sarcoma: A Case

Fatima Zahra Mrabet et al. Case Rep Pulmonol. .

Abstract

Primary pleuropulmonary synovial sarcoma is extremely rare. The diagnosis can only be made after having eliminated an extrapleuropulmonary localization in the past and at the time of diagnosis. Our presentation is about a 40-year-old woman having a cough and dyspnea since three weeks ago; imaging had showed a left pleurisy with pleuropulmonary process. Histological study of the biopsy confirmed the diagnosis of pleuropulmonary synovial sarcoma. PET-SCAN had not identified any extrathoracic localization. This tumor is known for its aggressive nature and high risk of metastasis. Its primitive character is retained following a diagnostic procedure of exclusion. Surgical treatment remains the best therapeutic tool when it is technically feasible; otherwise the prognosis is often unfortunate. In this paper, we report a case of primary pleuropulmonary synovial sarcoma. Through this case, we present a rare disease that is often difficult to diagnose.

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Figures

Figure 1
Figure 1
Posteroanterior chest roentgenogram showing a homogeneous opacity taking the whole hemi thoracic left field and pushing the mediastinum towards the contralateral side.
Figure 2
Figure 2
CT scan image showing a left mediastinal-pulmonary tumor process [(a) mediastinal window. (b) Parenchymal window].
Figure 3
Figure 3
Histologically, (a) the tumor showed spindle-shaped cells forming sheets (Hematoxylin Eosin GX10), (b) the spindle cells are of uniform appearance with oval, dark-staining nuclei and scanty amount of indistinct cytoplasm (Hematoxylin Eosin GX20), and (c) we noted a myxoid pattern (Hematoxylin Eosin GX10).
Figure 4
Figure 4
On immunohistochemical study, tumor cells were positive for EMA (a) and CD 99 (b).
See this image and copyright information in PMC

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