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Case Reports
. 2018 May 12;6(5):848-850.
doi: 10.3889/oamjms.2018.176. eCollection 2018 May 20.

A Very Rare Case of Cor Triatriatum with Severe Mitral Regurgitation

Selman Dumani  1 , Ermal Likaj  1 , Edlira Ruci  1 , Ervin Bejko  1 , Ali Refatllari  1
Affiliations
Case Reports

A Very Rare Case of Cor Triatriatum with Severe Mitral Regurgitation

Selman Dumani et al. Open Access Maced J Med Sci. .

Abstract

Background: Cor triatriatum sinister is rare congenital heart disease. It is mainly presented in childhood and often accompanied with other congenital anomalies. The cases with cor triatriatum treated surgically in adults and accompanied with severe mitral regurgitation are very rare.

Case report: We present a case with diagnosed cor triatriatum and severe mitral regurgitation. The diagnose was made by echocardiography. She was a female 25 years that was hospitalised with signs of heart failure NYHA II-III.

Conclusion: We performed the resection of the membrane in the left atrium and repair of a mitral valve according to Alfieri. The patient did very well after the surgery.

Keywords: Congenital heart disease; Cor triatriatum; Mitral regurgitation.

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Figures

Figure 1
Figure 1
LV-Left ventricle, RV-right ventricle, LAD-left atrium distal chamber, LAU-left atrium upper chamber. Between LAU and LAD, we can distinguish the membrane in the left atrium
Figure 2
Figure 2
(A) Cor triatriatum defect without any associated atrial septal defect; (B) Operative exposure of cor triatriatum membrane through a left atriotomy. Restrictive communication between the proximal and the distal left atrial chambers is visible; (C) Exposure of mitral valve after the excision of cor triatriatum membrane (arrows mark the line of excision Ann Thorac Surg 2014; 97:1659–63)
Figure 3
Figure 3
After we opened LA we see the membrane that divided LA into two parts upper and distal parts. Between four forceps has located the membrane. Between the right forceps is located the hole of the membrane of Cor Triatriatum
See this image and copyright information in PMC

References

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