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Case Reports
. 2018 Apr 25;31(3):350-351.
doi: 10.1080/08998280.2018.1446877. eCollection 2018 Jul.

Hemophagocytic lymphohistiocytosis

Jasmine Gowarty  1 , Julie Oda  2 , Christian Cable  2
Affiliations
Case Reports

Hemophagocytic lymphohistiocytosis

Jasmine Gowarty et al. Proc (Bayl Univ Med Cent). .

Abstract

Hemophagocytic lymphohistiocytosis (HLH) is a rare syndrome of widespread inflammation due to massive amounts of cytokines released from activated macrophages. The most common trigger for HLH is infection from a virus, most commonly Epstein-Barr virus. Here we report an adult case of this rare and life-threatening syndrome.

Keywords: Epstein-Barr virus; Kikuchi-Fujimoto disease; hemophagocytic lymphohistiocytosis; hemophagocytosis; parvovirus B19.

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