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Case Reports
. 2017 Apr-Jun;16(2):162-167.
doi: 10.1590/1677-5449.009416.

Tratamento endovascular de aneurisma de aorta abdominal com erosão de vértebra lombar associada à doença de Behçet: relato de caso

[Article in Portuguese]
Affiliations
Case Reports

Tratamento endovascular de aneurisma de aorta abdominal com erosão de vértebra lombar associada à doença de Behçet: relato de caso

[Article in Portuguese]
Nathalia Leslie Albanez Rodrigues de Souza et al. J Vasc Bras. 2017 Apr-Jun.

Abstract

Abstract: Behçet’s disease is an autoimmune, multifactorial, systemic condition with several clinical manifestations, including vascular disorders. An aortic aneurysm with vertebral erosion is rare in association with this pathology and there are only four case reports listed on the PubMed database. This article reports the case of a female patient with a long-standing diagnosis of Behçet’s Disease who developed a saccular infrarenal abdominal aortic aneurysm with lumbar vertebral erosion. Her surgical treatment consisted of endovascular repair with a monoiliac endoprosthesis and a femorofemoral crossover bypass, because of limitations imposed by the anatomy of the aortic bifurcation. This paper discusses the rarity of this presentation of the disease and treatment outcomes and offers a brief review of the relevant literature.

A doença de Behçet é uma doença sistêmica, multifatorial e autoimune com diversas manifestações clínicas, entre elas o acometimento vascular. Aneurisma de aorta associado a erosão de vértebra lombar é condição rara na literatura, existindo apenas quatro relatos de caso nas bases de dados da PubMed. O presente artigo relata o caso de paciente do sexo feminino com diagnóstico de Doença de Behçet de longa data e aneurisma sacular de aorta abdominal infrarrenal com erosão de vértebra lombar. O caso foi tratado por meio de técnica endovascular com colocação de endoprótese monoilíaca e enxerto fêmoro-femoral cruzado, devido a limitações anatômicas da bifurcação aórtica. O artigo aborda a raridade desse tipo de apresentação da doença e o desfecho do tratamento e apresenta revisão da literatura sobre esse tema.

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Conflict of interest statement

Conflito de interesse: Os autores declararam não haver conflitos de interesse que precisam ser informados.

Figures

Figura 1
Figura 1. Corte axial de angiotomografia pré-operatória mostrando o aneurisma de aorta com erosão da vértebra lombar.
Figura 2
Figura 2. Corte sagital de angiotomografia pré-operatória mostrando o aneurisma de aorta com erosão da vértebra lombar.
Figura 3
Figura 3. Corte axial de angiotomografia pós-operatória mostrando a endoprótese no interior do saco aneurismático, com exclusão do mesmo, sem evidência de endoleak.
Figura 4
Figura 4. Corte sagital de angiotomografia pós-operatória mostrando a endoprótese no interior do saco aneurismático, com exclusão do mesmo e sem evidência de endoleak.
Figura 5
Figura 5. Reconstrução 3-D em software Osirix® mostrando a endoprótese monoilíaca e o enxerto fêmoro-femoral cruzado pérvio e sem evidência de pseudoaneurismas.
Figure 1
Figure 1. Preoperative axial angiotomography showing aortic aneurysm with erosion of lumbar vertebra.
Figure 2
Figure 2. Preoperative sagittal angiotomography showing aortic aneurysm with erosion of lumbar vertebra.
Figure 3
Figure 3. Postoperative axial angiotomography showing endoprosthesis within the aneurysm sac, excluding it, with no evidence of endoleaks.
Figure 4
Figure 4. Postoperative sagittal angiotomography showing endoprosthesis within the aneurysm sac, excluding it, with no evidence of endoleaks.
Figure 5
Figure 5. 3-D reconstruction produced with Osirix® software, showing monoiliac endoprosthesis and femorofemoral crossover graft, patent and with no evidence of pseudoaneurysms.

References

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