Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Review
. 2018 Nov;29(6):714-716.
doi: 10.5152/tjg.2018.18596.

Primary intestinal lymphangiectasia and a review of the current literature

Zeynep Altın  1 , Yusuf Atabay  1 , Serhat Özer  2 , Miray Karakoyun  3 , Sümeyye Ekmekçi  4 , Ezgi Yıldız Yürekli  1 , Harun Akar  1
Affiliations
Review

Primary intestinal lymphangiectasia and a review of the current literature

Zeynep Altın et al. Turk J Gastroenterol. 2018 Nov.
No abstract available

PubMed Disclaimer

Conflict of interest statement

Conflict of Interest: The authors have no conflict of interest to declare.

Figures

Figure 1
Figure 1
Edema at distal part of the extremities
Figure 2
Figure 2
Endoscopic features
Figure 3
Figure 3
Dilated lymphatics (H&E, ×200), Positive staining with D2-40 immunohistochemistry in lymphatics (x200) in the duodenum mucosa
See this image and copyright information in PMC

References

    1. Levitt DG, Levitt MD. Protein losing enteropathy: comprehensive review of the mechanistic association with clinical and subclinical disease states. Clin Exp Gastroenterol. 2017;10:147–68. - PMC - PubMed
    1. Vignes S, Bellanger J. Primary intestinal lymphangiectasia (Waldmann’s disease) Orphanet J Rare Dis. 2008;3:5. - PMC - PubMed
    1. Le Bougeant P, Delbrel X, Grenouillet M, Leou S, Djossou F, Beylot J, et al. Familial Waldmann’s disease. Ann Med Interne. 2000;151:511–2. - PubMed
    1. Hennekam RC, Geerdink RA, Hamel BC, Hennekam FA, Kraus P, Rammeloo JA, et al. Autosomal recessive intestinal lymphangiectasia and lymphedema, with facial anomalies and mental retardation. Am J Med Genet. 1989;34:593–600. https://doi.org/10.1002/ajmg.1320340429 - DOI - PubMed
    1. Ozeki M, Fukao T, Kondo N. Propranolol for intractable diffuse lymphangiomatosis - PubMed

LinkOut - more resources