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Case Reports
. 1987;73(3):295-300.
doi: 10.1007/BF00686625.

Variability of morphological features in early infantile polyneuropathy with defective myelination

A Vital, C Vital, J P Riviere, C Brechenmacher, J Marot
Case Reports

Variability of morphological features in early infantile polyneuropathy with defective myelination

A Vital et al. Acta Neuropathol. 1987.

Abstract

Four cases of early infantile polyneuropathy with defective myelination are reported. The peripheral nerve was studied by light and electron microscopy; different morphological characteristics have been noticed in these patients. Case 1 presented aspects of defective myelination with atypical "onion bulb" formation composed of multiple layers of basement membrane. In case 2, defective myelination and atypical "onion bulb" formation were associated with aberrant hypermyelination. Cases 3 and 4 were brothers, who presented axonal damage and atypical "onion bulb" formation.

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References

    1. Arch Neurol. 1977 Jun;34(6):337-45 - PubMed
    1. J Neurol Neurosurg Psychiatry. 1985 Dec;48(12):1269-76 - PubMed
    1. Acta Neuropathol. 1974 Feb 28;27(2):105-18 - PubMed
    1. Neuropediatrics. 1983 Aug;14(3):182-3 - PubMed
    1. Pediatrie. 1978 Mar;33(2):201-7 - PubMed

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