Otosclerosis and Dysplasias of the Temporal Bone

Abstract

Many bone dysplasias, some common and others rare, may involve the temporal bone causing conductive, sensorineural, or mixed hearing loss, vestibular dysfunction, or skull base foraminal narrowing, potentially affecting quality of life. Some conditions may affect only the temporal bone, whereas others may be more generalized, involving different regions of the body. High-resolution computed tomography may detect subtle osseous changes that can help define the type of dysplasia, and MR imaging can help define the degree of activity of lesions and potential associated complications.

Keywords: Bone dysplasia; Fibrous dysplasia; Osteogenesis imperfecta; Osteopetrosis; Otosclerosis; Paget disease.