Laugier-Hunziker Syndrome

Excerpt

Laugier-Hunziker syndrome, also known as Laugier-Gerbig-Hunziker syndrome, Laugier-Hunziker-Baran syndrome, or idiopathic lenticular mucocutaneous pigmentation, is a hereditary pigmentary disorder characterized by a unique expression of pigmentation over the mucosal, nail, and acral sites. The condition is known to be benign; nevertheless, a few associations with esophageal melanocytosis, actinic lichen planus, hypocellular bone marrow, and thrombocytopenia have been reported. Due to its close resemblance to more serious conditions such as Addison's disease, Peutz-Jeghers syndrome, Cronkhite-Canada syndrome, and lentiginosis profuse, this is usually classified as an exclusion diagnosis.