Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2019 Feb;41(2):124-128.
doi: 10.1055/s-0038-1676110. Epub 2018 Dec 12.

Imaging Description of Extragenital Müllerian Adenosarcoma: A Case Report

Affiliations
Case Reports

Imaging Description of Extragenital Müllerian Adenosarcoma: A Case Report

Annalisa Mone et al. Rev Bras Ginecol Obstet. 2019 Feb.

Abstract

Müllerian adenosarcoma is a very rare gynecological disease, comprising 5% of uterine sarcomas. Extragenital localizations are even rarer. We report a very interesting case of a 27-year-old woman complaining of pelvic pain, with a subsequent diagnosis of extragenital Müllerian adenosarcoma. This is the first case reported in the literature with a complete and wide imaging description. Even if rare, Müllerian adenosarcoma should be hypothesized in case of young female patients presenting with suspicious pelvic mass.

O adenosarcoma Mülleriano é uma doença ginecológica muito rara, compreendendo 5% dos sarcomas uterinos. Localizações extragenitais são ainda mais raras. Relatamos um caso muito interessante de uma mulher de 27 anos queixando-se de dor pélvica com diagnóstico subsequente de adenosarcoma Mülleriano extragenital. Este é o primeiro caso relatado na literatura com uma descrição completa e ampla de imagem. Mesmo que raro, o adenosarcoma Mülleriano deve ser hipotetizado no caso de pacientes jovens do sexo feminino com massa pélvica suspeita.

PubMed Disclaimer

Conflict of interest statement

None to declare.

Figures

Fig. 1
Fig. 1
Copious ascites on transabdominal ultrasound (A) and CECT (B).
Fig. 2
Fig. 2
Transabdominal ultrasound (A) and axial CECT (B-C) images show a large solid, heterogeneous mass containing cystic spaces (▸). Note the presence of calcifications (→) (C).
Fig. 3
Fig. 3
Mass shows internal vascularity on ultrasound color Doppler (A) and axial computed tomography during arterial phase (B-C) (→). Enhancing on venous/portal phase of septa and pseudosepta (D) (→).

References

    1. Guidozzi F, Smith T, Koller A B, Reinecke L. Management of uterine Müllerian adenosarcoma with extrauterine metastatic deposits. Gynecol Oncol. 2000;77(03):464–466. - PubMed
    1. Abeler V M, Røyne O, Thoresen S, Danielsen H E, Nesland J M, Kristensen G B.Uterine sarcomas in Norway. A histopathological and prognostic survey of a total population from 1970 to 2000 including 419 patients Histopathology 20095403355–364. Doi: 10.1111/j.1365-2559.2009.03231.x - PubMed
    1. McCluggage W G.Mullerian adenosarcoma of the female genital tract Adv Anat Pathol 20101702122–129. Doi: 10.1097/PAP.0b013e3181cfe732 - PubMed
    1. D'Angelo E, Prat J.Uterine sarcomas: a review Gynecol Oncol 201011601131–139. Doi: 10.1016/j.ygyno.2009.09.023 - PubMed
    1. Patrelli T S, Gizzo S, Di Gangi S, Guidi G, Rondinelli M, Nardelli G B.Cervical Mullerian adenosarcoma with heterologous sarcomatous overgrowth: a fourth case and review of literature BMC Cancer 201111236 Doi: 10.1186/1471-2407-11-236 - PMC - PubMed

Publication types

Supplementary concepts

LinkOut - more resources