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Case Reports
. 2018 Dec;8(6):537-540.
doi: 10.1212/CPJ.0000000000000509.

Foix-Chavany-Marie syndrome as the presenting sign of HIV-related PML

Femke Dijkstra  1 , Kaat Guldolf  1 , Katlijn Schotsmans  1 , Emke Maréchal  1 , Danielle Hernalsteen  1 , Roeland Crols  1
Affiliations
Case Reports

Foix-Chavany-Marie syndrome as the presenting sign of HIV-related PML

Femke Dijkstra et al. Neurol Clin Pract. 2018 Dec.
No abstract available

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Figures

Figure 1
Figure 1. MRI findings
Cerebral MRI with typical progressive multifocal leukoencephalopathy (PML) lesions. A fluid-attenuated inversion recovery sequence shows (A) a focal hyperintense signal in the subcortical white matter and involvement of immediate subcortical U fibers in the left hemisphere (arrow) with an old subcortical toxoplasmosis lesion contralateral and (B) no abnormalities in the brainstem or cerebellum. A diffusion-weighted imaging (DWI) sequence (C) shows accompanying diffusion restriction (arrow). A follow-up DWI sequence after 2 months (D) shows important extension of the left lesion with mass effect, suggestive for PML–immune reconstitution inflammatory syndrome, and appearance of a new PML lesion in the right opercular region (arrow).
Figure 2
Figure 2. Cerebral motor function representation
Cerebral MRI with the progressive multifocal leukoencephalopathy lesion (arrow) on a coronal fluid-attenuated inversion recovery sequence, with a homunculus superimposed that shows the motor representation of different regions within the primary motor cortex. The affected region represents the facial motor function.
See this image and copyright information in PMC

References

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