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Case Reports
. 2018 Dec 13:8:Doc07.
doi: 10.3205/oc000089. eCollection 2018.

Oguchi's disease with Mizuo-Nakamura phenomenon in a seven-year-old boy

Pukhraj Rishi  1 , Ekta Rishi  1 , Sharanya Abraham  1
Affiliations
Case Reports

Oguchi's disease with Mizuo-Nakamura phenomenon in a seven-year-old boy

Pukhraj Rishi et al. GMS Ophthalmol Cases. .

Abstract

A seven-year-old boy presented with difficulty in night vision of five years duration. Vision was 20/20 OU. Fundus examination revealed a golden sheen over the posterior pole in both eyes which disappeared after 45 minutes of dark adaptation, suggestive of Mizuo-Nakamura phenomenon. Clinical findings were suggestive of Oguchi's disease. ERG was confirmatory.

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Conflict of interest statement

The authors declare that they have no competing interests.

Figures

Figure 1
Figure 1. Fundus photos of the right (A) and left (B) eye reveal a golden sheen caused by the Mizuo-Nakamura phenomenon. The golden sheen is extinguished after 45 minutes of dark adaptation as seen in the fundus photos of the right (C) and left (D) eye.
Figure 2
Figure 2. ERG showing the negative waveform morphology with non-recordable single flash rod response, negative-positive combined response, and normal photopic response
See this image and copyright information in PMC

References

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