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. 2018 Dec 2:2018:5081540.
doi: 10.1155/2018/5081540. eCollection 2018.

Congenital Midline Cervical Cleft and W-Plasty: Our Experience

Abdullah Bahakim  1   2 , Martine Francois  1 , Thierry Van Den Abbeele  1
Affiliations

Congenital Midline Cervical Cleft and W-Plasty: Our Experience

Abdullah Bahakim et al. Int J Otolaryngol. .

Abstract

Objectives: Congenital midline cervical cleft (CMCC) is a very uncommon congenital anomaly of the midline anterior neck, and although it has very pathognomonic features (including nipple-like protuberance), it could be mistaken for other congenital neck lesions, such as thyroglossal duct cyst and branchial apparatus anomalies. Thus, it represents a challenging diagnosis. In this 21-patient series, we discuss the clinical features of CMCC, its pathophysiology characteristics, and its modalities management.

Material and methods: We conducted a retrospective chart review of children presenting with CMCC at our institution, between January 1998 and January 2016.

Results: Twenty-one patients were identified with CMCC. Ages ranged between 1 day and 14 years. The length of the lesion varied from 0.5 to 5 cm, and the size of the skin tag varied from 0.2 to 1.5cm. No other significant associated anomalies were found. Surgery was the mainstay treatment, and no recurrence was found. W-plasty was used in most patients to close the defect.

Conclusion: With a little more than 200 published cases, our series represents the largest series worldwide. The lesion is usually isolated, and no further investigation is required. Surgery is the mainstay of treatment, with complete excision being usually curative. It should be treated at an early age to prevent complications. In our experience, W-plasty was a good alternative to the most commonly used Z-plasty, in skin closure, with respect to both aesthetic and functional results.

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Figures

Figure 1
Figure 1
Clinical criteria of CMCC: superior nipple-like structure, inferior sinus, and atrophic skin in between.
Figure 2
Figure 2
Perioperative view showing the excision of the CMCC.
Figure 3
Figure 3
W-plasty after wound closure.
Figure 4
Figure 4
CMCC in a 2-year-old boy.
Figure 5
Figure 5
Postoperative result in the same patient at 12 months.
Figure 6
Figure 6
18-month postoperative result in the same patient in Figure 4.
See this image and copyright information in PMC

References

    1. Von Luschka H. Ueber fistula colli congenita. Archiv für Physiologische Heilkunde. 1848;7:24–27.
    1. Bailey H. Thyroglossal cysts and fistulæ. British Journal of Surgery. 1925;12(47):579–589. doi: 10.1002/bjs.1800124716. - DOI
    1. Tessier P. Anatomical classification of facial, cranio facial and latero facial cleft. Journal of Maxillofacial Surgery. 1976;4(2):69–92. doi: 10.1016/S0301-0503(76)80013-6. - DOI - PubMed
    1. Mlynarek A., Hagr A., Tewfik T. L., Nguyen V. H. Congenital mid-line cervical cleft: Case report and review of literature. International Journal of Pediatric Otorhinolaryngology. 2003;67(11):1243–1249. doi: 10.1016/s0165-5876(03)00201-5. - DOI - PubMed
    1. Gargan T. J., McKinnon M., Mulliken J. B. Midline cervical cleft. Plastic and Reconstructive Surgery. 1985;76(2):225–229. doi: 10.1097/00006534-198508000-00008. - DOI - PubMed

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