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. 2019 Apr;29(2):255-256.
doi: 10.1007/s10286-019-00590-3. Epub 2019 Jan 12.

Improvement of daytime hypercapnia with nocturnal non-invasive ventilation in familial dysautonomia

Horacio Kaufmann  1 , Lucy Norcliffe-Kaufmann  2 , Jose-Alberto Palma  2
Affiliations

Improvement of daytime hypercapnia with nocturnal non-invasive ventilation in familial dysautonomia

Horacio Kaufmann et al. Clin Auton Res. 2019 Apr.
No abstract available

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Figures

Fig. 1
Fig. 1
Arterial blood gas concentrations during wakefulness (day-time) before (Pre-NIV) and after non-invasive ventilation (Post-NIV). Treatment with non-invasive ventilation in patients with familial dysautonomia resulted in significantly reduced arterial pCO2 concentration during daytime (P < 0.0001, left panel), suggesting that nocturnal non-invasive ventilation could reset the chemoreceptor during daytime. Nocturnal non-invasive ventilation did not change arterial pO2 levels (P = 0.1167, right panel)
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References

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