[Steinert's disease and conduction disorders. Apropos of a familial study]

Abstract

The authors reported a new family case of Steinert with twelve years follow-up. The study of potentials in the bundle of his was performed in all patients, showed an intra- and infra-hisian blocks. This study showed a discrepancy between muscular and myocardial evolutive injury, a very important knowledge for follow-up. Conduction disturbances were found in two cases and pacemaker insertion was performed in one patient. The authors specified the indication of electrophysiological studies during the onset and pacemaker implantation in all patient with a typical or suggestive history of syncope.