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. 2018 Dec;13(4):141-144.
doi: 10.1016/j.joto.2018.10.001. Epub 2018 Oct 11.

Conductive hearing loss in chronic inflammatory demyelinating polyneuropathy (CIDP): A case report

Mark A Fadel  1 , Kevin Y Zhan  2 , Edward E Dodson  2
Affiliations

Conductive hearing loss in chronic inflammatory demyelinating polyneuropathy (CIDP): A case report

Mark A Fadel et al. J Otol. 2018 Dec.

Abstract

Chronic inflammatory demyelinating polyneuropathy (CIDP) is a progressive autoimmune disorder that targets peripheral nerves. It commonly presents with motor-predominant dysfunction and enlargement of cranial nerves. With regards to hearing loss, a few cases of sensorineural loss have been described. We present a novel case of conductive hearing loss caused by a mass on the tympanic segment of the facial nerve in the setting of CIDP.

Keywords: Chronic inflammatory demyelinating polyneuropathy; Cranial neuropathy; Hearing loss; Ossicular erosion.

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Figures

Fig. 1
Fig. 1
Audiogram demonstrating conductive hearing loss. “O” = right unmasked air. “X” = left unmasked air. “[“ = right masked bone. “]“ = left masked bone.
Fig. 2
Fig. 2
Post contrast axial T1-weighted MRI demonstrating bilaterally thickened tympanic segments of the facial nerve (arrows). a: Non-contrast axial CT scan showing bilaterally enlarged fallopian canals in the mastoid segment (white arrows), as well as dilated foramen ovale (red arrow). b: Non-contrast axial CT scan showing ossicular erosion secondary to enlarged tympanic segment of the facial nerve.
Fig. 3
Fig. 3
Intraoperative finding of the soft tissue mass (*) just medial to the chorda tympani nerve (Chorda). The photo is in surgical position, with the left side of the photo as inferior and top half of the photo as anterior. There is a small piece of surgical packing anteroinferiorly. “RW” = round window. “Promontory” = cochlear promontory.
See this image and copyright information in PMC

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