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Case Reports
. 2019 Jan 19:26:200-202.
doi: 10.1016/j.rmcr.2019.01.013. eCollection 2019.

Chest wall lipoblastoma in a 3 year-old boy

Maria Parisi  1 , Efthimia Grenda  1 , Elpis Hatziagorou  1 , George Tsikopoulos  2 , Christophoros N Foroulis  3 , Vasiliki Georgopoulou  4 , Athanasia Anastasiou  4 , Eleni Tsiviki  5 , John Tsanakas  1
Affiliations
Case Reports

Chest wall lipoblastoma in a 3 year-old boy

Maria Parisi et al. Respir Med Case Rep. .

Abstract

Background: Lipoblastoma is a rare, benign, fatty tissue tumor that occurs in infancy and early childhood. The most common tumor locations are the extremities and the torso. The location of this tumor in the chest wall and an intrathoracic extension is uncommon.

Case report: We present a case of a 3-year-old boy with anterior chest wall lipoblastoma with an intrathoracic extension. Computed tomography was suggestive of lipoblastoma. The mass was completely excised through a right posterolateral thoracotomy. The histologic examination of the lesion confirmed the diagnosis of lipoblastoma.

Conclusion: Although extremely rare, chest wall lipoblastoma should be included in the differential diagnosis of thoracic mass in childhood.

Keywords: Chest wall; Children; Lipoblastoma; Thoracic mass.

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Figures

Fig. 1
Fig. 1
Chest X-Ray: There is a giant soft tissue, well-demarcated, lobulated mass in the right hemithorax expanding and splaying the adjacent ribs.
Fig. 2
Fig. 2
Contrast enhanced CT Images in axial and coronal planes show a large predominantly fatty mass containing thick internal enhancing septations with some nodularity. The mass is situated in the right posterolateral thoracic wall and is seen to be invading between the ribs with extension into the overlying muscles of the thoracic wall.
Fig. 3
Fig. 3
MRI scan with i.v. contrast demonstrate a large heterogeneous heterogenous mass that is predominantly isointense relative to subcutaneous fat in all sequences. Inside the mass there are thick septations probably representing fibrous tissue. There are also areas of soft tissue attenuation and with high signal intensity on T2 WI probably representing myxoid tissue (arrow).
See this image and copyright information in PMC

References

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