Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2016 May-Aug;4(2):125-128.
doi: 10.4103/1658-631X.178350. Epub 2016 Mar 9.

Psammomatoid Ossifying Fibroma of the Ethmoid Sinus with Secondary Intracranial Aneurymal Bone Cyst: A Case Report and Literature Review

Salma S Al-Sharhan  1 , Mona M Ashoor  1 , Areej M Al-Nemer  2
Affiliations
Case Reports

Psammomatoid Ossifying Fibroma of the Ethmoid Sinus with Secondary Intracranial Aneurymal Bone Cyst: A Case Report and Literature Review

Salma S Al-Sharhan et al. Saudi J Med Med Sci. 2016 May-Aug.

Abstract
in English, Arabic

Juvenile psammomatoid ossifying fibroma (JPOF) is a rare, slowly progressive tumor of the extragnathic craniofacial bones, with a tendency toward locally aggressive behavior and recurrence. The pathognomonic histopathologic feature is the presence of spherical ossicles, which are similar to psammoma bodies. Very few cases in association with secondary aneurysmal bone cyst (ABC) formation have been reported in literature. Treatment consists of complete surgical removal. However, incomplete excision has been associated with a high local recurrence rate. The prognosis is good because malignant change and metastasis have not been reported. The authors are reporting a case of JPOF of the ethmoid bones with secondary ABC in a 7-year-old female patient.

ملخص البحث : الورم الليفي الرملي العظمي من الحالات النادرة وهو ورم بطئ النمو داخل الجمجمة وذو طبيعة متكررة. يعرض الباحثون حالة لطفلة تبلغ من العمر7 سنوات تم تشخيصها بهذا الورم في الجيب ألغربالي داخل الجمجمة. وتم علاجها جراحيا باستئصال الورم كاملاً باستخدام المنظار.

Keywords: Aneurysmal bone cyst; endoscopic management; paranasal sinuses; psammomatoid ossifying fibroma.

PubMed Disclaimer

Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
(a-c) Different cross bonding views (axial, sagittal, and coronal) bone window computed tomography image shows an ellipticshape, well-defined, and mixed density mass with peripheral groundglass density arising from the left ethmoid sinus and pushing the left orbit out and down word.
Figure 2
Figure 2
(a) Sagittal T1-weighted image shows isointense signal of peripheral ossifying fibroma (OF). (b and c) Peripheral remnant OF has hypointense signal, and aneurysmal bone cyst (ABC) shows multicystic, heterogeneous signal intensity with multiple fluid-fluid levels on the axial T2-weighted image. (d) Axial contrast-enhanced T1-weighted image with fat saturation shows moderate enhancement of OF and, septal and peripheral enhancement of ABC.
Figure 3
Figure 3
Left carotid arteriogram shows all the branches with no uptake by the mass.
Figure 4
Figure 4
Intraoperative endoscopic view with navigation guided after the complete excision of the mass.
Figure 5
Figure 5
Microscopic picture shows the psammomatoid bodies embedded in a fibrous stroma (×100).
See this image and copyright information in PMC

Similar articles

See all similar articles

Cited by

References

    1. Waknisa P, Sarodeb SC, Dolasa RS. Psammomatoid juvenile ossifying fibroma of the mandible with secondary aneurysmal bone cyst: A case report. Asian J Oral Maxillofac Surg. 2011;2:83–6.
    1. El-Mofty S. Psammomatoid and trabecular juvenile ossifying fibroma of the craniofacial skeleton: Two distinct clinicopathologic entities. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2002;93:296–304. - PubMed
    1. Slootweg PJ, Panders AK, Koopmans R, Nikkels PG. Juvenile ossifying fibroma: An analysis of 33 cases with emphasis on histopathological aspects. J Oral Pathol Med. 1940;23:385–8. - PubMed
    1. Sarode SC, Sarode GS, Waknis P, Patil A, Jashika M. Juvenile psammom`: A review. Oral Oncol. 2011;47:1110–6. - PubMed
    1. Johnson LC, Yousefi M, Vinh TN, Heffner DK, Hyams VJ, Hartman KS. Juvenile active ossifying fibroma. Its nature, dynamics and origin. Acta Otolaryngol Suppl. 1991;488:1–40. - PubMed

Publication types