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Comment
. 2019 May 1;199(9):1053-1054.
doi: 10.1164/rccm.201903-0696ED.

Unraveling the CFTR Function-Phenotype Connection for Precision Treatment in Cystic Fibrosis

Edith T Zemanick  1 , Deepika Polineni  2
Affiliations
Comment

Unraveling the CFTR Function-Phenotype Connection for Precision Treatment in Cystic Fibrosis

Edith T Zemanick et al. Am J Respir Crit Care Med. .
No abstract available

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References

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    1. Accurso FJ, Van Goor F, Zha J, Stone AJ, Dong Q, Ordonez CL, et al. Sweat chloride as a biomarker of CFTR activity: proof of concept and ivacaftor clinical trial data. J Cyst Fibros. 2014;13:139–147. - PMC - PubMed
    1. McKone EF, Velentgas P, Swenson AJ, Goss CH. Association of sweat chloride concentration at time of diagnosis and CFTR genotype with mortality and cystic fibrosis phenotype. J Cyst Fibros. 2015;14:580–586. - PubMed
    1. Rowe SM, Verkman AS. Cystic fibrosis transmembrane regulator correctors and potentiators. Cold Spring Harb Perspect Med. 2013;3:pii: a009761. - PMC - PubMed

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