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Review
. 2018 Oct 3:31:76.
doi: 10.11604/pamj.2018.31.76.17107. eCollection 2018.

[Verneuil's disease: a diagnosis that should be taken into consideration in patients with vulvar and perineal tumor-like lesion]

[Article in French]
Anis Haddad  1 , Olfa Zoukar  1 , Sonia Hammami  1
Affiliations
Review

[Verneuil's disease: a diagnosis that should be taken into consideration in patients with vulvar and perineal tumor-like lesion]

[Article in French]
Anis Haddad et al. Pan Afr Med J. .

Abstract
in English, French

We here report the case of a 58-year old nulliparous patient with a history of Niemann-Pick disease who presented with vulvoperineal, fluctuant, fistulized swelling measuring 10 cm associated with ulceration. The patient was febrile with impaired general state This mass caused some concern about necrotic and infected malignant tumor of the vulva associated with chronic dermatosis. Incision and purulent drainage associated with multiple biopsies excluded the presence of a neoplastic process. The diagnosis of suppurative hidradenitis or Verneuil's disease was based on the associations between lesions and their distributions. Then, the problem that arose was that of the choice between drug treatment and surgical procedures. This study, including a short review of the recent literature, aims to outline the diagnostic modalities, the complications and the therapeutic management of this disease.

Les auteurs rapportent le cas d'une patiente de 58 ans, nulligeste, aux antécédents de maladie de Niemann-Pick qui a consulté pour une tuméfaction vulvo-périnéale de 10 cm, fluctuante et fistulisé avec une ulcération. La patiente était fébrile et présentant un état général altéré. Cette masse a fait craindre le développement d'une tumeur maligne vulvaire nécrosée et infectée sur une dermatose chronique. Elle a eu une incision en vue de drainage des collections purulentes associée à des biopsies multiples qui ont infirmé la présence d'un processus néoplasique. L'association lésionnelle et leurs distributions ont fait porter alors le diagnostic d'une hidradenite suppurative ou maladie de Verneuil. Ensuite le problème posé était celui du choix de la conduite de prise en charge ultérieure parmi les traitements médicamenteux et chirurgicaux décrits. Les auteurs discuteront à travers ce cas et une brève revue de la littérature récente les modalités du diagnostic, les complications et la prise en charge thérapeutique de cette maladie.

Keywords: Suppurative hidradenitis; clinical diagnosis; complications; treatment; vulvar cancer.

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Conflict of interest statement

Les auteurs ne déclarent aucun conflit d'intérêts.

Figures

Figure 1
Figure 1
Masses nodulaires vulvo-périnéales
Figure 2
Figure 2
Volumineuse masse vulvaire gauche
Figure 3
Figure 3
Lésions des plis fessiers et des faces internes des cuisses
See this image and copyright information in PMC

References

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