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Case Reports
. 2019 Apr 26:25:100898.
doi: 10.1016/j.eucr.2019.100898. eCollection 2019 Jul.

Rare case of primary bladder Wilm's tumor in a 1-year old boy

Jufriady Ismy  1 , Jufitriani Ismy  2 , Reno Kamarlis  3 , Akhmad Mustafa  4
Affiliations
Case Reports

Rare case of primary bladder Wilm's tumor in a 1-year old boy

Jufriady Ismy et al. Urol Case Rep. .

Abstract

Extrarenal Wilms' tumor (EWRT) is a rare entity, but primary bladder Wilm's tumor is even rarer with only 1 case reported. A 1-year old boy came with chronic urinary retention. Abdominal pelvic CT scan revealed intravesical mass arising from anterior bladder wall extending to the prostate and bladder neck. Initial cystoscopic diagnosis revealed chronic granuloma. We decided to perform partial cystectomy with final pathologic result of bladder Wilms' tumor. EWRT may occur in various organs, but primary bladder Wilms' tumor is extremely rare case.

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Figures

Fig. 1
Fig. 1
Abdominal-pelvic CT scan revealed dilatation of in left pelvocalyceal system, and mass inside the bladder from anterior bladder wall extending to the prostate and bladder neck.
Fig. 2
Fig. 2
(a) and (b) intraoperative findings of partial cystectomy, (c) Histopathologic finding revealed Small blue cells were arranged in serpiginous aggregates (blastemal component) and primitive neuroepithelial cells between fibromyxoid tissues. (d) Primitive neuroepithelial cells.
Fig. 3
Fig. 3
a. blastemal component (100x with HE); b. stromal component (40x, with HE); c. Enlarged hyperchromatic nucleus; d. Epithelial component (40x, HE).
See this image and copyright information in PMC

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