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Case Reports
. 2019 Jun;67(6):942-943.
doi: 10.4103/ijo.IJO_192_19.

Multimodal retinal imaging of a 6-year-old male child with incontinentia pigmenti

Alok Sen  1 , Pratik Shenoy  1 , Ashish Mitra  1 , Tanya Jain  1
Affiliations
Case Reports

Multimodal retinal imaging of a 6-year-old male child with incontinentia pigmenti

Alok Sen et al. Indian J Ophthalmol. 2019 Jun.
No abstract available

Keywords: Foveal hypoplasia; OCT angiography; incontinentia pigmenti.

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Conflict of interest statement

None

Figures

Figure 1
Figure 1
Clinical photograph showing facial pigmentation on the cheeks and sparse, wiry hair, and hypopigmentation along Blaschko's lines
Figure 2
Figure 2
Fundus picture at presentation showing gliosis over the disc, macular pseudohole (yellow circle) with superotemporal neovascularization (asterisk) and avascular retina (a). FFA at presentation shows the small FAZ, pin point leaks at the site of aneurysms (arrowhead), and leakage at the site of neovascularization with extensive CNP superotemporally (b)
Figure 3
Figure 3
OCT at presentation shows the ERM, inner layer loss at the macula (arrowhead). In addition, it demonstrates the loss of retinal architecture temporal to the fovea (arrow) with retinal thinning (a). OCTA shows the superotemporal flow voids in the region of retinal ischemia (hashtag) with a small FAZ in the superficial and deep capillary plexus (asterisk) (b)
Figure 4
Figure 4
Fundus picture 4 months post laser shows regression of the retinal neovascularization with fibrous proliferation and laser scars
See this image and copyright information in PMC

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References

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