Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2019 Jun;67(6):944-945.
doi: 10.4103/ijo.IJO_417_19.

Retinal imaging in incontinentia pigmenti

Subina Narang  1 , Meenakshi Sindhu  1 , Suksham Jain  1 , Jitender Jinagal  1
Affiliations
Case Reports

Retinal imaging in incontinentia pigmenti

Subina Narang et al. Indian J Ophthalmol. 2019 Jun.
No abstract available

Keywords: Fundus fluorescein angiography; vasculature in incontinentia pigmenti.

PubMed Disclaimer

Conflict of interest statement

None

Figures

Figure 1
Figure 1
Multiple grayish-brown vesiculopapular skin lesions visible on the flexor aspects of limbs and sides of the abdomen
Figure 2
Figure 2
Dilated fundus photograph of the (a) right and (b) left eyes showing tortuous and dilated vessels (black arrowheads) at posterior pole along with large vascular loops in zone 1. (b) There was the presence of Roth spots (black arrow) and multiple flame-shaped hemorrhages (white arrow) as well
Figure 3
Figure 3
(a and b) FFA photographs of right eye: The retinal arteries were seen only till posterior to the equator with large mid-peripheral vascular loops (white arrows). There was gross peripheral capillary nonperfusion and peripapillary capillary plexus could be seen for about two to four discs diameter (arrowheads). (c) Late phase shows leakage from the disc (white arrows)
Figure 4
Figure 4
FFA photographs of the left eye show similar findings like large nonperfused area, vascular loops (a) and Roth spots (b) as right eye
Figure 5
Figure 5
(a) Right eye developed vitreous hemorrhage (arrow) and retinal detachment (arrowhead) during follow-up period. (b) Left eye shows regressed neovascularization with scatter laser marks (arrow) with attached retina (arrowhead)
See this image and copyright information in PMC

Similar articles

See all similar articles

Cited by

  • Avascular Peripheral Retina in Infants.
    Özdek Ş, Özdemir Zeydanlı E, Baumal C, Hoyek S, Patel N, Berrocal A, Lopez-Cañizares A, Al-Khersan H, Kusaka S, Mano F, Jalali S, Lepore D, Akar S. Özdek Ş, et al. Turk J Ophthalmol. 2023 Feb 24;53(1):44-57. doi: 10.4274/tjo.galenos.2022.76436. Turk J Ophthalmol. 2023. PMID: 36847634 Free PMC article. Review.

References

    1. Carney RG. Incontinentia pigmenti. A world statistical analysis. Arch Dermatol. 1976;112:535–42. - PubMed
    1. Minic S, Trpinac D, Obradovi’c M. Incontinentia pigmenti diagnostic’criteria update. Clin Genet. 2014;85:536–42. - PubMed
    1. Chen CJ, Han IC, Goldberg MF. Variable expression of retinopathy in a pedigree of patients with incontinentia pigmenti. Retina. 2015;35:2627–32. - PubMed
    1. Tzu JH, Murdock J, Parke DW, 3rd, Warman R, Hess DJ, Berrocal AM. Use of fluorescein angiography in incontinentia pigmenti: A case report. Ophthalmic Surg Lasers Imaging Retina. 2013;44:91–3. - PubMed

Publication types