Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
. 2019 May 23;11(2):7951.
doi: 10.4081/pr.2019.7951.

Special-needs patients in pediatric dentistry: Progeroid syndrome. A case of dental management and oral rehabilitation

Maria Grazia Cagetti  1 , Nicole Camoni  1 , Flavia Cetraro  1 , Massimo Scanferla  1 , Giacomo Maria Moretti  1
Affiliations

Special-needs patients in pediatric dentistry: Progeroid syndrome. A case of dental management and oral rehabilitation

Maria Grazia Cagetti et al. Pediatr Rep. .

Abstract

This report presents a case of an eightyear- old girl affected by a progeroid syndrome of unclear genetic origins. The patient's dental history included oligodontia, premature deciduous exfoliation and roots abnormalities. She was treated with comprehensive oral rehabilitation using dentures. Oral health instructions were given during the whole treatment and follow- up period. The goal of improving the masticatory function and the esthetic was achieved, allowing the patient to increase her social abilities and self-confidence.

Keywords: Pediatric dentistry; dental anomalies; oral rehabilitation; progeroid syndrome.

PubMed Disclaimer

Conflict of interest statement

Conflict of interest: the authors declare no potential conflict of interest.

Figures

Figure 1.
Figure 1.
X-rays and pictures before and after the oral rehabilitation.
Figure 2.
Figure 2.
Upper and lower dentures and intra-oral pictures before and after the insertion of the dentures.
See this image and copyright information in PMC

References

    1. Sinha JK, Ghosh S, Raghunath M. Progeria: a rare genetic premature ageing disorder. Indian J Med Res 2014;139:667-74. - PMC - PubMed
    1. Carrero D, Soria-Valles C, López-Otín C. Hallmarks of progeroid syndromes: lessons from mice and reprogrammed cells. Dis Model Mech. 2016;9:719-35. - PMC - PubMed
    1. Wiedemann HR. An unidentified neonatal progeroid syndrome: followup report. Eur J Pediatr 1979;130:65-70. - PubMed
    1. Rastogi R, Chander Mohan SM. Progeria syndrome: a case report. Indian J Orthop 2008;42:97-9. - PMC - PubMed
    1. Delgado-Luengo WN, Petty EM, Solís-Añez E, et al. Petty-Laxova- Wiedemann progeroid syndrome: further phenotypical delineation and confirmation of a rare syndrome of premature aging. Am J Med Genet A 2009;149A:2200-5. - PubMed