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Case Reports
. 2019 Jul 2;12(7):e228410.
doi: 10.1136/bcr-2018-228410.

A rare case of hyperammonaemic encephalopathy

Yeu Jye Pang  1 , Stephanie Day  1 , Daniel Sumner  2 , Kenneth Adegoke  1
Affiliations
Case Reports

A rare case of hyperammonaemic encephalopathy

Yeu Jye Pang et al. BMJ Case Rep. .

Abstract

A 75-year-old female patient presented to the accident and emergency department following a collapse. She was treated for a saddle pulmonary embolism and underlying urinary tract infection. However, 48 hours later she was found to have reduced consciousness with no apparent cause (Glasgow Coma Scale of 8 out of 15). Subsequent blood results revealed a highammonia level. After reflection into her medical history, it was found that she had bladder exstrophy, which was managed with urinary diversion surgery as an infant, and her presentation was a rare complication of this operation.

Keywords: congenital disorders; surgery; urological surgery.

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Conflict of interest statement

Competing interests: None declared.

Figures

Figure 1
Figure 1
CT abdomen and pelvis scan demonstrating the course of the left ureter with its anastomosis to the sigmoid colon.
Figure 2
Figure 2
CT abdomen and pelvis scan demonstrating a fluid-filled colonic neobladder.
Figure 3
Figure 3
Diagram illustrating diversion of the ureters to the colon as a result of urinary diversion surgery. Illustrated by Yeu Jye Pang.
See this image and copyright information in PMC

References

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