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Case Reports
. 2019 Jan-Jun;9(1):208-210.
doi: 10.4103/ams.ams_281_18.

Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up

Naveenkumar Jayakumar  1 , Veerabahu Rathnaprabhu  2 , Singaravelu Ramesh  3
Affiliations
Case Reports

Preliminary Report of a True NasoMaxillary Infantile Fibrosarcoma: Single-Modality Management and 2-Year Follow-Up

Naveenkumar Jayakumar et al. Ann Maxillofac Surg. 2019 Jan-Jun.

Abstract

Infantile fibrosarcoma (IFS) is a malignant tumor, commonly presenting in long bones and seldom encountered after 2 years of age. It is extremely rare in the faciomaxillary region. The condition is often mistaken for teratomas, and histopathology/immunohistochemistry is confirmatory. Treatment involves surgical resection as primary modality. Prognosis is much better compared to the adult variant with even scope for spontaneous regression following "conservative" resection. We present a case of IFS of the nasomaxillary complex in a 3-month-old female child. We managed our case with surgical resection, and the patient has remained disease free for over 2 years.

Keywords: Fibroblastic tumor; hemangioma; infantile fibrosarcoma; teratoma.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Preoperative image showing nasomaxillary mass causing cheilo-nasal dysmorphism
Figure 2
Figure 2
(a) Preoperative magnetic resonance imaging showing soft-tissue mass in the nasomaxillary region. (b) Delivery of the excised mass. (c) Closure of the defect
Figure 3
Figure 3
Photomicrograph showing cellular spindle cell lesion arranged in fascicles with “herringbone pattern”
Figure 4
Figure 4
Photomicrograph showing vimentin positivity in neoplastic cells
Figure 5
Figure 5
Eighteen months’ postoperative follow-up showing complete regain of facial architecture
See this image and copyright information in PMC

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