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Review
. 2019 Dec 1;58(23):3393-3400.
doi: 10.2169/internalmedicine.3094-19. Epub 2019 Jul 22.

Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review

Masayoshi Ko  1 , Kenya Kamimura  1 , Akira Sakamaki  1 , Yusuke Niwa  1 , Kentaro Tominaga  1 , Kenichi Mizuno  1 , Shuji Terai  1
Affiliations
Review

Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review

Masayoshi Ko et al. Intern Med. .

Abstract

Fibromuscular dysplasia (FMD) and segmental arterial mediolysis (SAM) are noninflammatory, nonatherosclerotic arterial diseases that cause aneurysm, occlusion, and thromboses. These diseases are rarely seen in mesenteric arterial lesions; however, as they can be lethal if appropriate management is not provided, the accumulation of clinical information from cases is essential. We herein report the cases of a 57-year-old man diagnosed with FMD and a 63-year-old man diagnosed with SAM. We conclude that an early diagnosis with imaging modalities and clinical information followed by the appropriate treatment improves the prognosis of these arterial diseases.

Keywords: fibromuscular dysplasia; diagnosis; mesenteric lesion; segmental arterial mediolysis.

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Conflict of interest statement

The authors state that they have no Conflict of Interest (COI).

Figures

Figure 1.
Figure 1.
Imaging studies of FMD in Case 1. (a, b, c) Computed tomography (CT) and three-dimensional reconstruction showed stenosis (red arrows), aneurysmal changes (red arrowheads), and partially dissection (black arrowheads in a and b) in the superior mesenteric artery. (d, e) Stenosis (red arrows) and aneurysmal changes (red arrowheads) in the branch of the right renal artery. Magnetic resonance angiography showed stenosis (red arrows) and aneurysmal changes (red arrowheads) in the left vertebral artery (f). FMD: fibromuscular dysplasia
Figure 2.
Figure 2.
Imaging studies of SAM in Case 2. (a, b, c) Computed tomography (CT) and three-dimensional reconstruction showed bleeding in the abdominal cavity (red arrows) and dissecting aneurysm (red arrowheads) in the celiac artery to splenic artery. (d, e, f) The bilateral external iliac arteries showed multiple aneurysmal changes (red arrowheads) and partial dissection (black arrowheads in d and e). SAM: segmental arterial mediolysis
See this image and copyright information in PMC

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