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Case Reports
. 2019 Summer;13(3):113-120.

Juvenile Clinically Amyopathic Dermatomyositis: A Case Report and Review of Literature

Vadood Javadi Parvaneh  1 , Mehrdad Yasaei  1 , Khosro Rahmani  1 , Yalda Nilipour  2
Affiliations
Case Reports

Juvenile Clinically Amyopathic Dermatomyositis: A Case Report and Review of Literature

Vadood Javadi Parvaneh et al. Iran J Child Neurol. 2019 Summer.

Abstract

Juvenile clinically amyopathic dermatomyositis (juvenile CADM) is a rare rheumatologic disease in children defined as the presence of the hallmark cutaneous features of dermatomyositis in absence of muscle involvement. In this article, we report an Iranian 14.5-year-old girl presented to Rheumatology Clinic of Mofid Children's Hospital, Tehran, Iran in Jan 2016 with cutaneous complaints diagnosed with juvenile CADM. Finally, we provide a literature review of previous studies on juvenile CADM.

Keywords: Children; Dermatomyositis sine myositis; Juvenile clinically amyopathic dermatomyositis; Juvenile dermatomyositis; pediatrics.

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Conflict of interest statement

Author declare that they have no conflict of interest.

Figures

Figure 1
Figure 1
Muscle MRI showed no abnormal signal
Figure 2
Figure 2
Skin biopsy showed mild lichenoid reaction and perivascular chronic inflammatory cell infiltration of dermal layer and some epidermotropism and no spongiosis
Figure 3
Figure 3
Muscle biopsy showed slight fiber variation and no necrosis/regeneration and perifascicular atrophy
See this image and copyright information in PMC

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