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Case Reports
. 2019 Jun 8:18:e20180121.
doi: 10.1590/1677-5449.180121.

Endovascular treatment for Behçet's disease: a case report

Sergio Quilici Belczak  1   2 , Ingredy Tavares da Silva  1 , Gustavo Garcia Marques  1 , Letícia Flores Copetti  1 , Vanessa Stefaniak  1 , Gustavo Gomes Quintas  1 , Kaique Bernardo Uchimura  1
Affiliations
Case Reports

Endovascular treatment for Behçet's disease: a case report

Sergio Quilici Belczak et al. J Vasc Bras. .

Abstract
in English, Portuguese

Behçet's disease (BD) is a multisystemic vasculitis of unknown etiology. Cardiovascular involvement has been thoroughly described in the literature and the major cause of death in BD is secondary to aneurysm complications. In this case report, a patient with BD presented with a recurrent abdominal aortic aneurysm, which was corrected using a custom-made endoprosthesis. The optimal treatment for patients with BD remains highly controversial and challenging because of technical difficulties and frequent recurrence. Endovascular intervention seems to be a feasible alternative with considerably less morbidity than conventional surgery.

Resumo: A doença de Behçet (DB) é uma vasculite multissistêmica de etiologia desconhecida. O acometimento cardiovascular é bem descrito na literatura, sendo que a principal causa de morte na DB é secundária a complicações aneurismáticas. Relata-se aqui o caso de um paciente portador de DB com aneurisma de aorta abdominal reincidente, o qual foi corrigido por meio de endoprótese customizada. O tratamento ideal para portadores de DB ainda é bastante controverso e desafiador, tendo em vista as dificuldades técnicas e as recidivas frequentes. A intervenção endovascular apresenta-se como uma alternativa viável e consideravelmente menos mórbida do que a cirurgia convencional.

Keywords: Behçet syndrome; endovascular procedures; stents, aneurysm.

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Conflict of interest statement

No conflicts of interest declared concerning the publication of this article.

Figures

Figure 1
Figure 1. Initial angiography before placement of the second endoprosthesis.
Figure 2
Figure 2. Control angiography after deployment of the second endoprosthesis and the covered stents.
Figure 3
Figure 3. Three-dimensional reconstruction of control angiotomography at 6-month follow-up.
Figura 1
Figura 1. Angiografia inicial antes do implante da segunda endoprótese.
Figura 2
Figura 2. Angiografia de controle após o implante da segunda endoprótese e dos stents revestidos.
Figura 3
Figura 3. Reconstrução tridimensional da angiotomografia de controle do paciente após 6 meses de evolução.
See this image and copyright information in PMC

References

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