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Case Reports
. 2019 Jun 3;7(7):1362-1364.
doi: 10.1002/ccr3.2243. eCollection 2019 Jul.

Unilateral segmental Darier's disease associated with neuropsychiatric disorders

Luke Horton  1 , Darius Mehregan  2
Affiliations
Case Reports

Unilateral segmental Darier's disease associated with neuropsychiatric disorders

Luke Horton et al. Clin Case Rep. .

Abstract

Unilateral segmental Darier's disease (DD) is a rare variant of DD that presents with erythematic lesions in a unilateral distribution without other associated features of DD. Although diagnosis is challenging, unilateral segmental DD should be considered for an acantholytic dermatosis in a unilateral distribution and a history of neuropsychiatric disorders.

Keywords: Darier's disease; Grover's disease; Hailey‐Hailey.

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Conflict of interest statement

None declared.

Figures

Figure 1
Figure 1
Hyperkeratotic erythematous papules confined to the right side of the body following lines of Blaschko
Figure 2
Figure 2
Histopathologic examination shows suprabasilar acantholysis, corps ronds and grains (hematoxylin‐eosin, original magnification × 25)
Figure 3
Figure 3
Histopathologic examination shows suprabasilar acantholysis, corps ronds and grains (hematoxylin‐eosin, original magnification × 100)
See this image and copyright information in PMC

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