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Case Reports
. 2019 Apr-Jun;29(2):75-77.
doi: 10.4103/jcecho.jcecho_69_18.

Challenges with Managing Delayed Presentation of Persistent Truncus Arteriosus with Torrential Pulmonary Blood Flow in a Resource-Limited Setting

Affiliations
Case Reports

Challenges with Managing Delayed Presentation of Persistent Truncus Arteriosus with Torrential Pulmonary Blood Flow in a Resource-Limited Setting

Igoche David Peter et al. J Cardiovasc Echogr. 2019 Apr-Jun.

Abstract

Embryologically, incomplete conotruncal septation with resultant single aortopulmonary trunk and defective ventricular septation defines the congenital cardiac lesion known as persistent truncus arteriosus (PTA). Torrential pulmonary blood flow is inevitable when this rare lesion is further compounded by patency of the arterial ductus. Such was the case of a patient who presented with fast breathing, reduced suck, darkening of the tongue, and extremities. Urgent echocardiographic diagnosis was PTA (Type A1) with patent ductus arteriosus and pulmonary hypertension and left ventricular systolic dysfunction.

Keywords: Patent ductus arteriosus; persistent truncus arteriosus; torrential pulmonary blood flow.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Parasternal short-axis view showing a single truncal vessel with confluent pulmonary arteries branching posteriorly
Figure 2
Figure 2
Parasternal long-axis view showing malaligned ventricular septal defect with an overriding single truncal vessel
Figure 3
Figure 3
Patent ductus arteriosus with nonrestrictive left to right flow on continuous-wave Doppler
Figure 4
Figure 4
Elevated peak tricuspid regurgitant velocity on continuous-wave Doppler

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