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Case Reports
. 2019 Nov;23(7):e13567.
doi: 10.1111/petr.13567. Epub 2019 Aug 13.

Sub-acute neonatal hemochromatosis in an infant with hypoplastic left heart syndrome on ventricular assist device awaiting transplantation

Hanna J Tadros  1   2 , Dipankar Gupta  1 , Megan Childress  1   2 , Genie Beasley  3 , Ashlie E Rubrecht  4 , Archana Shenoy  4 , Joseph Philip  1 , Mark S Bleiweis  1 , Desiree S Machado  1
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Case Reports

Sub-acute neonatal hemochromatosis in an infant with hypoplastic left heart syndrome on ventricular assist device awaiting transplantation

Hanna J Tadros et al. Pediatr Transplant. 2019 Nov.

Abstract

Single-ventricle pediatric patients, amongst other children waiting for OHT, are a vulnerable population, especially if candidacy is established before any palliation. NH is a rare disease with poor prognosis in the post-natal period. We present a case of sub-acute NH diagnosed in an infant with HLHS who was listed for OHT while bridged with a pulsatile paracorporeal VAD, with an emphasis on the evolution of the condition throughout the patient's clinical course and the ultimate decision for compassionate deactivation of VAD.

Keywords: gestational alloimmune liver disease; heart transplantation; hypoplastic left heart syndrome; sub-acute neonatal hemochromatosis; ventricular assist device.

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References

REFERENCES

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