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. 2019 Jun 23;7(8):1617-1618.
doi: 10.1002/ccr3.2282. eCollection 2019 Aug.

Electrical storm in an acquired short QT syndrome successfully treated with quinidine

Michael Spartalis  1 , Efthimios Livanis  1 , Eleftherios Spartalis  2 , Alexandros Tsoutsinos  3
Affiliations

Electrical storm in an acquired short QT syndrome successfully treated with quinidine

Michael Spartalis et al. Clin Case Rep. .

Abstract

Short QT syndrome (SQTS) is a malignant heart disorder defined by the presence of ventricular arrhythmias causing syncope and sudden cardiac arrest. The prevalence in the pediatric population is 0.05%. Quinidine is an established agent for pharmacological prophylaxis in SQTS patients, but can also terminate an electrical storm.

Keywords: arrhythmia; electrical storm; quinidine; short QT.

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Conflict of interest statement

The authors report no financial relationships or conflicts of interest regarding the content herein.

Figures

Figure 1
Figure 1
The 12‐lead surface electrocardiogram (ECG) obtained on the admission showed sinus rhythm with a heart rate of 60 bpm, a QT of 320 ms and a QTc of 320 ms
Figure 2
Figure 2
ECG strip showing an episode of Torsade de pointes degenerate into ventricular fibrillation. The episode was induced after a premature ventricular beat due to R/T phenomenon
See this image and copyright information in PMC

References

    1. Pereira R, Campuzano O, Sarquella‐Brugada G, et al. Short QT syndrome in pediatrics. Clin Res Cardiol. 2017;106(6):393‐400. - PubMed
    1. Campuzano O, Sarquella‐Brugada G, Cesar S, Arbelo E, Brugada J, Brugada R. Recent advances in short QT syndrome. Front Cardiovasc Med. 2018;5:149. - PMC - PubMed

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