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Case Reports
. 2019 Aug 28;12(8):e229371.
doi: 10.1136/bcr-2019-229371.

Ossifying fibromyxoid tumor: a rare case

Masood Umer  1 , Javeria Saeed  1 , Nasir Ud Din  2 , Kiran Hilal  3
Affiliations
Case Reports

Ossifying fibromyxoid tumor: a rare case

Masood Umer et al. BMJ Case Rep. .

Abstract

Ossifying fibromyxoid tumour (OFMT) is a rarely occurring soft tissue neoplasm of mesenchymal origin. It is a rarely found tumour with intermediate behaviour and differentiation. Although it is mostly benign, malignant variants also exist. We are presenting a case of 32-year-old man presented in clinic with complaints of painless swelling in left distal thigh. After reviewing his X-ray, a diagnostic biopsy was planned which came out to be suspicious of solitary fibrous tumour. Other radiological workup was done and the patient was planned to undergo wide margin excision. The final histopathology showed a diagnosis of OFMT of soft tissue, atypical variant. The patient is under follow-up and is disease free. This type of tumour possesses potential of local recurrence and metastases; therefore, it is important to keep a long-term follow-up of patient.

Keywords: orthopaedic and trauma surgery; surgical oncology.

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Conflict of interest statement

Competing interests: None declared.

Figures

Figure 1
Figure 1
X-ray left femur.
Figure 2
Figure 2
MRI left knee.
Figure 3
Figure 3
Preoperative preparation.
Figure 4
Figure 4
Excised specimen.
Figure 5
Figure 5
Histology of resected specimen.
Figure 6
Figure 6
Immunohistochemical stains S100, CD56 and desmin.
Figure 7
Figure 7
Post 6 months of surgery.
See this image and copyright information in PMC

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