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Case Reports
. 2019 May 31;3(4):171-176.
doi: 10.1016/j.case.2019.04.005. eCollection 2019 Aug.

A Vicious Circle: Heyde Syndrome in Mild Aortic Stenosis

Johannes P Schwaiger  1 , Othmar Ludwiczek  1 , Ivo Graziadei  1 , Wilhelm Grander  1
Affiliations
Case Reports

A Vicious Circle: Heyde Syndrome in Mild Aortic Stenosis

Johannes P Schwaiger et al. CASE (Phila). .
No abstract available

Keywords: Aortic stenosis; Heyde Syndrome; High-output cardiac failure; von Willebrand factor.

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Figures

None
Graphical abstract
Figure 1
Figure 1
Echocardiogram demonstrating significant but proportional dilatation of all cardiac chambers. (A) The left ventricular end-diastolic volume was 230 mL (indexed 85 mL). (B) The tricuspid anulus was 4.78 cm, and the basal right ventricular diameter was 5.89 cm. (C) The left atrial area was 38 cm² (indexed 14 cm²). (D) The right atrial area was 33.2 cm² (indexed 12 cm²).
Figure 2
Figure 2
Pulsed-wave Doppler across mitral valve demonstrating near normal filling of left ventricle.
Figure 3
Figure 3
Pulsed-wave Doppler right upper pulmonary vein demonstrating near normal filling of left atrium.
Figure 4
Figure 4
M-Mode aortic valve demonstrating good opening of aortic valve.
Figure 5
Figure 5
Continuous-wave Doppler signal across aortic valve demonstrating a maximum velocity of 3.7 m/sec and a mean gradient of 36.9 mm Hg.
Figure 6
Figure 6
Planimetric measurement of aortic valve orifice (2.4 cm2) during transesophageal echocardiography.
Figure 7
Figure 7
Angiodysplastic vessels in the small intestines seen in capsule endoscopy.
Figure 8
Figure 8
Multimeric analysis of plasma demonstrating a deficiency of large von Willebrand multimers at presentation, which completely resolved after aortic valve replacement.
See this image and copyright information in PMC

References

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