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Case Reports
. 2019 Nov;36(11):2122-2125.
doi: 10.1111/echo.14497. Epub 2019 Oct 1.

The strange case of congenital mitral stenosis in an adult man with cor triatriatum

Maria Livia Burzo  1 , Giuseppe De Matteis  1 , Maria Anna Nicolazzi  1 , Elisa Fedele  2   3 , Davide Antonio Della Polla  1 , Faustino Pennestrì  2 , Angela Maria Rita Favuzzi  1
Affiliations
Case Reports

The strange case of congenital mitral stenosis in an adult man with cor triatriatum

Maria Livia Burzo et al. Echocardiography. 2019 Nov.

Abstract

We report the case of a 74-year-old male, with a medical history of cor triatriatum, admitted with a 10-day history of intermittent fever. Three sets of blood cultures were positive for Providencia rettgeri. Transthoracic and transesophageal echocardiogram excluded infective endocarditis, but revealed a congenital accessory tissue adhering to the mitral valve, causing supravalvular mitral stenosis. Cor triatriatum sinistrum is a rare congenital cardiac anomaly, even more uncommon in adults, and quite exceptional when associated with mitral valve disease. Because the patient had no symptoms related to the heart valve disease, no surgical indication was given and he was managed conservatively.

Keywords: congenital heart disease; cor triatriatum; doppler echocardiography; mitral stenosis; three-dimensional echocardiography.

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References

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