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Case Reports
. 2019 Oct;7(2):147-150.
doi: 10.14791/btrt.2019.7.e40.

A Case of Sporadic Suprasellar Hemangioblastoma Mimicking Meningioma

Byung Moo Kang  1 , Sang Min Youn  2
Affiliations
Case Reports

A Case of Sporadic Suprasellar Hemangioblastoma Mimicking Meningioma

Byung Moo Kang et al. Brain Tumor Res Treat. 2019 Oct.

Abstract

Hemangioblastoma (HBL) in the suprasellar region is very rare and a few cases have been reported. Suprasellar HBL without von Hippel-Lindau disease is much rarer. A 76-year old male patient presented progressively deteriorating visual disturbance. MRI demonstrated solid suprasellar mass of 20 mm in diameter, broadly based to planum sphenoidale and diaphragm sella and dural tail sign after the administration of gadolinium diethylene triamine penta-acetic acid (Gd-DTPA). Preoperative diagnosis was meningioma. Total resection of the tumor was not accomplished because of massive hemorrhage, and the histopathologic examination revealed the tumor to be HBL. The visual disturbance of the patient was not improved. The authors reviewed the literature and considered a differential diagnosis of suprasellar tumors and treatment of suprasellar HBL.

Keywords: Hemangioblastoma; Suprasellar; von Hippel Lindau disease.

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Conflict of interest statement

The authors have no potential conflicts of interest.

Figures

Fig. 1
Fig. 1. Preoperative axial MRI without contrast enhancement showing isointense on T1-weighted image and hyperintense on T2-weighted image suprasellar mass of 20 mm in diameter (A and B). Sagittal and coronal image with contrast enhancement demonstrated homogeneously enhancing solid mass broadly based to planum sphenoidale and diaphragm sella and strong dural tail sign (arrow) (C and D).
Fig. 2
Fig. 2. Hematoxylin and eosin staining showing two different components characterized by numerous thin walled capillary vessels and stromal cells, which are characteristically clear and vacuolated cytoplasm were seen in low and high magnification [×200 (A), ×400 (B)]. Immunostaining for CD34 highlighted the rich vascular network (C) and stromal cells showed immunoreactivity for neuron specific enolase (D).
See this image and copyright information in PMC

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