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. 2019 Nov;71(Suppl 3):1757-1761.
doi: 10.1007/s12070-017-1100-y. Epub 2017 Feb 8.

Binder's Syndrome: A Case Report

Rohit Mehrotra  1 , Pankaj Srivastava  2 , Anubhaw Katiyar  3
Affiliations

Binder's Syndrome: A Case Report

Rohit Mehrotra et al. Indian J Otolaryngol Head Neck Surg. 2019 Nov.

Abstract

Binder's syndrome or nasomaxillary hypoplasia or maxillonasal dysplasia is an uncommon developmental disorder predominantly affecting the maxillary anterior region and the nasal complex. A concave profile, broad and flat nose, short columella, convex upper lip, and malocclusion are the major clinical findings. The characteristic features of this syndrome are developmental failure in the premaxillary area, with concomitant defects of the nasal skeleton. The current article presents case report of 16 year old patient of binder's syndrome describing its features, surgical intervention and postop results.

Keywords: Binder′s syndrome; Maxillary hypoplasia; Maxillonasal dysplasia; Pre maxilla depression; Rib cartilage.

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Conflict of interest statement

Conflict of interestSince there are no funding issues all three authors declares that there is no conflict of interest.

Figures

Fig. 1
Fig. 1
Pre op image
Fig. 2
Fig. 2
Removal of rib cartilage
Fig. 3
Fig. 3
Placement of rib cartilage with screws in pre maxilla
Fig. 4
Fig. 4
Placement of septal cartilage
Fig. 5
Fig. 5
Post op image
Fig. 6
Fig. 6
After 5 days postop
Fig. 7
Fig. 7
Post op images after two weeks
Fig. 8
Fig. 8
X-ray showing intact maxillary screws
See this image and copyright information in PMC

References

    1. Quarrell OW, Koch M, Hughes HE. Maxillonasal dysplasia (Binder’s syndrome) J Med Genet. 1990;27:384–387. doi: 10.1136/jmg.27.6.384. - DOI - PMC - PubMed
    1. Nedev PK. The binder syndrome: review of the literature and case report. Internet J Neurosurg. 2008;5:1–4. - PubMed
    1. Hopkin GB. Hypoplasia of the middle third of the face associated with congenital absence of the anterior nasal spine, depression of the nasal bones, and angle class III malocclusion. Br J Plast Surg. 1963;16:146–153. doi: 10.1016/S0007-1226(63)80097-1. - DOI - PubMed
    1. Couly G. Embryogenesis and malformations of the face and of the neck] Med Foet Echo Gynecol. 2000;44:42–55.
    1. Cormier-Sedaire V. Face and bony dysplasia. Med Foet Echo Gynecol. 2000;44:28–29.

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