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. 2020 Sep/Oct;36(5):438-443.
doi: 10.1097/IOP.0000000000001589.

Morbihan Syndrome, a UK Case Series

Camille Yvon  1 , Hardeep Singh Mudhar  2 , Tessa Fayers  3 , We Fong Siah  4 , Raman Malhotra  5 , Zanna Currie  6 , Jennifer Tan  6 , Saul Rajak  1
Affiliations

Morbihan Syndrome, a UK Case Series

Camille Yvon et al. Ophthalmic Plast Reconstr Surg. 2020 Sep/Oct.

Abstract

Purpose: To describe 10 patients with Morbihan syndrome, a rare condition characterized by the slow appearance of erythema and solid edema on the upper portion of the face, and review the literature.

Methods: Retrospective case series and review.

Results: The majority of patients were male (80%), and the mean age at presentation was 67 years (range, 48-88 years); 60% had asymmetrical disease (affecting mainly the right side). All subjects underwent a lid biopsy to support the diagnosis of Morbihan syndrome, which showed features of inflammation and vascular dysfunction, highly suggestive of a rosacea histological picture complicated by chronic lymphoedema. A range of medical and surgical treatment were used with variable success. The most effective ones included oral isotretinoin, intralesional triamcinolone injections, and debulking surgery.

Conclusions: Morbihan syndrome is a rare and chronic condition. It can be difficult to treat and may require a range of interventions.

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References

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