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. 2021 Feb;22(1):13-19.
doi: 10.1007/s40368-020-00508-y. Epub 2020 Jan 31.

Oral health of Brazilian individuals with mucopolyssaccaridosis

T D Deps  1 , E C França  2 , E R Valadares  3 , B Nicolau  4 , I A Pordeus  5 , A C Borges-Oliveira  6
Affiliations

Oral health of Brazilian individuals with mucopolyssaccaridosis

T D Deps et al. Eur Arch Paediatr Dent. 2021 Feb.

Abstract

Purpose: This study described and compared the oral characteristics of Brazilian individuals with mucopolysaccharidosis (MPS) and without MPS.

Methods: A cross-sectional study was performed with 29 individuals with MPS and 29 without MPS and their parents/guardians. The individuals were aged between 3 and 21 years and attended at two hospitals in Belo Horizonte, southeastern Brazil. The dental characteristics were evaluated by clinical examination of dental caries, gingivitis, malocclusion, dental anomalies and developmental defects of enamel. The parents/guardians answered a questionnaire about the sociodemographic and behavioural aspects of their children. The study was approved by the Research Ethics Committee of the Federal University of Minas Gerais.

Results: The average age of the individuals was 13.9 years (± 7.2). The majority were male (58.6%), had black/brown skin (70.7%) and were from favored economic class (89.7%). Dental caries, gingivitis, malocclusion and dental anomalies were more prevalent in the MPS group (p < 0.05).

Conclusion: The individuals with MPS had a higher prevalence of oral diseases and dental anomalies than the group without MPS.

Keywords: Dental care for disabled; Dental caries; Malocclusion; Mucopolysaccharidosis; Oral health; Rare disease.

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