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. 2020 Dec;34(12):2345-2346.
doi: 10.1038/s41433-020-0792-5. Epub 2020 Feb 10.

Use of optical coherence tomography angiography in the diagnosis of small retina lesions in Von Hippel-Lindau disease

Lindsay Y Chun  1 , Nathalie Massamba  1 , Megan R Silas  1 , Michael P Blair  1 , Seenu M Hariprasad  1 , Dimitra Skondra  2   3
Affiliations

Use of optical coherence tomography angiography in the diagnosis of small retina lesions in Von Hippel-Lindau disease

Lindsay Y Chun et al. Eye (Lond). 2020 Dec.
No abstract available

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Conflict of interest statement

The authors declare that they have no conflict of interest.

Figures

Fig. 1
Fig. 1. Case 1 - OCTA confirms presence of a retinal angioma in a VHL patient with equivocal findings on fundus photo and FFA.
Fundus photo (a larger image), FFA (a upper left corner), and en face OCTA images (b) of the subclinical retinal angioma in Case 1. Fluorescein angiography (a) shows an area of hyperfluorescence below the inferior arcade not seen in the fundus image or exam. En face OCTA imaging (b) of that area confirms the presence of a retinal angioma with blood flow.
Fig. 2
Fig. 2. Case 2 - OCTA confirms absence of angiomatous lesion in a VHL patient with irregular lesion seen on FA and FAF but not fundus photo.
Fundus autofluorescence (a), color fundus photo (b larger image), FFA (b upper left corner), en face OCTA images (c) in Case 2. Fundus photo (b) of the inferior retina is unremarkable, but the fundus autofluorescence (a) and FFA (b upper left corner) highlighted an inferotemporal irregularity concerning for a subclinical small angioma. Further assessment with OCTA (c) did not show evidence of a vascular lesion.
See this image and copyright information in PMC

References

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