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. 2020 Jan 31:13:21-22.
eCollection 2020.

Rare Association of Absent Pulmonary Valve Syndrome with Double Outlet Right Ventricle and Hypoplastic Left Heart Complex

Erik L Frandsen  1 , Arpan R Doshi  2 , Sujatha Buddhe  1 , Bhawna Arya  1 , Sathish M Chikkabyrappa  1
Affiliations

Rare Association of Absent Pulmonary Valve Syndrome with Double Outlet Right Ventricle and Hypoplastic Left Heart Complex

Erik L Frandsen et al. Kans J Med. .
No abstract available

Keywords: double outlet right ventricle; hypoplastic left heart syndrome; pulmonary valve; ventricular heart septal defects.

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Figures

Figure 1
Figure 1
Transverse axial 2-D still frame of a fetal echocardiogram demonstrated the absent pulmonary valve with severely dilated main and branch pulmonary arteries. PV: pulmonary valve; LPA: left pulmonary artery; RPA: right pulmonary artery; RV: right ventricle.
Figure 2
Figure 2
Transthoracic echocardiogram in apical view demonstrated severely hypoplastic non-apex forming left ventricle (LV), dilated right ventricle (RV) and severely dilated pulmonary artery (PA).
Figure 3
Figure 3
Parasternal short axis view of transthoracic echocardiogram demonstrating severely dilated aneurysmal main and branch pulmonary arteries and dysplastic and rudimentary pulmonary valve. RPA - right pulmonary artery; LPA - left pulmonary artery; RVOT - right ventricular outflow tract; PV - pulmonary valve; PA - pulmonary artery.
See this image and copyright information in PMC

References

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    1. Forrest P, Bini RM, Wilkinson JL, et al. Congenital absence of the pulmonic valve and tricuspid valve atresia with intact ventricular septum. Am J Cardiol. 1987;59(5):482–484. - PubMed
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