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. 2020 Mar;15(1):1-5.
doi: 10.1016/j.joto.2019.06.001. Epub 2019 Jul 3.

Transcanal endoscopic assisted skull base endolymphatic sac tumor resection: A rare disease with advanced technology

Affiliations

Transcanal endoscopic assisted skull base endolymphatic sac tumor resection: A rare disease with advanced technology

Wai Tsz Chang et al. J Otol. 2020 Mar.

Erratum in

Abstract

Endolymphatic sac tumors (ELSTs) are rare, papillary adenomatous tumors that arise from the endothelium of the endolymphatic sac. We demonstrate a difficult case of endolymphatic sac tumor and how it is managed via transcanal endoscopic assisted technique, with discussion of feasibility of transcanal approach to lateral skull base tumor.

Keywords: Endolymphatic sac; Lateral skull base; Transcanal combined endoscopic microscopic approach; Transcanal endoscopic assisted technique.

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Figures

Fig. 1
Fig. 1
MRI showing pre-operative tumor involvement (IAM: Internal Acoustic meatus; LSCC: Lateral semicircular canal).
Fig. 2
Fig. 2
External incision of transcanal approach (EAC: External acoustic canal).
Fig. 3
Fig. 3
Tissue plane between tumor and dura with 4 K system (MCF: middle cranial fossa; PCF: posterior cranial fossa).
Fig. 4
Fig. 4
Endoscopic approach to Internal Acustic Meatus with curved instruments (PSCC: posterior semicircular canal; MCF: middle cranial fossa; IAM: internal acoustic meatus).
Fig. 5
Fig. 5
a: Low power magnification showing tumor fragments admixed both blood clot and fibrins. b: Higher power magnification showing papillary and glandular structures lined by a single layer of epithelium. c: High power magnification showing low grade nuclear features of tumor cells. d: Cytoderatin stain (AE1/AE3) highlights the lining cells. e: VHL stain were negative.
Fig. 6
Fig. 6
a,b: CT scan showing transcanal approach to Internal Acoustic Meatus and Jugular Bulb.
Fig. 7
Fig. 7
Intra-auricular wound, 2 weeks post op (EAC: External auditory canal).
Fig. 8
Fig. 8
Post operative 2 weeks external cosmetic appearance.

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