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Review
. 2020 May;27(5):1338-1347.
doi: 10.1245/s10434-020-08221-2. Epub 2020 Feb 28.

Update on Pheochromocytoma and Paraganglioma from the SSO Endocrine and Head and Neck Disease Site Working Group, Part 2 of 2: Perioperative Management and Outcomes of Pheochromocytoma and Paraganglioma

Dhaval Patel  1 , John E Phay  2 , Tina W F Yen  3 , Paxton V Dickson  4 , Tracy S Wang  3 , Roberto Garcia  5 , Anthony D Yang  6 , Lawrence T Kim  7 , Carmen C Solórzano  8
Affiliations
Review

Update on Pheochromocytoma and Paraganglioma from the SSO Endocrine and Head and Neck Disease Site Working Group, Part 2 of 2: Perioperative Management and Outcomes of Pheochromocytoma and Paraganglioma

Dhaval Patel et al. Ann Surg Oncol. 2020 May.

Abstract

This is the second part of a two-part review on pheochromocytoma and paragangliomas (PPGLs). In this part, perioperative management, including preoperative preparation, intraoperative, and postoperative interventions are reviewed. Current data on outcomes following resection are presented, including outcomes after cortical-sparing adrenalectomy for bilateral adrenal disease. In addition, pathological features of malignancy, surveillance considerations, and the management of advanced disease are also discussed.

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Figures

FIG. 1
FIG. 1
a Diagram outlining port placement for robotic retroperitoneoscopic approach to an adrenalectomy. b Patient prepped, draped, and ports placed for robotic retroperitoneal total adrenalectomy
FIG. 2
FIG. 2
Eleven-year-old male with VHL syndrome who underwent laparoscopic bilateral partial adrenalectomies guided with intraoperative ultrasound for bilateral pheochromocytomas. a Right adrenal tumor measuring 1.8 cm. b Post right partial adrenalectomy with preservation of the right adrenal vein. c Left adrenal tumor measuring 3.0 cm. d Post left partial adrenalectomy with preservation of the left adrenal vein. *Left and right adrenal tumors, respectively, ^Left and right adrenal veins, respectively, IVC inferior vena cava
FIG. 3
FIG. 3
A 59-year-old male with SDHB who underwent PRRT for progressive metastatic PPGL showing mild response after four cycles of treatment. a Baseline 68-gallium DOTATATE PET/CT scan showing widely metastatic disease. b 68-Gallium DOTATATE PET/CT scan showing mild tumor response after four cycles of Lutathera therapy
See this image and copyright information in PMC

References

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