[Right-side hypertrophic cardiomyopathies]

Abstract

A complex of clinicoinstrumental methods (two-dimensional and Doppler echocardiography, cardiac catheterization, etc.) was used for the detection of right heart hypertrophic cardiomyopathies (RHHCMP) (52 patients aged 16 to 67). Right heart local apical HCMP (20 patients) was characterized by regional hypertrophy (1.45 +/- 0.027 cm) and hypokinesia of the apical segment of the interventricular septum (IVS). Hypertrophy of the IVS second/third and RV apex, a RV peak-like shape on a ventriculogram were revealed in apical RHHCMP (17 patients). Obstructive asymmetric RHHCMP (3 patients) was manifested in a regular increase in the IVS thickness (2.2 +/- 0.17 cm) with the obstruction of the RV cavity. Regional hypertrophy of the IVS basal part (1.47 +/- 0.09 cm), moderate dilation of the right ventricle were observed in obstructive sigmoid RHHCMP (12 patients) with the obstruction of the orifice of the RV or of both ventricles. In some of the examinees RHHCMP was combined with a moderate rise of pulmonary arterial pressure of unknown genesis and with other congenital heart anomalies.