Papillary intralymphatic angioendothelioma: Dabska tumor

Abstract

Papillary intralymphatic angioendothelioma (Dabska tumor) is a rarely metastasizing lymphatic vascular neoplasm that usually affects children and young adults. The majority of these cases occur in soft tissues of extremities, and to date less than 40 cases have been described. Despite the generally indolent evolution, can be locally invasive with the potential to metastasize. We describe a case of a young woman presenting with a plantar lesion, for 9 months and histological diagnosis of Dabska tumor. This neoplasm should be considered in the differential diagnosis of vascular dermatoses, allowing early diagnosis and treatment. Long-term follow-up should be performed.

Keywords: Histology; Lymphatic vessel tumors; Neoplasms; Soft tissue neoplasms; Vascular tissue.

Figure 1

Violaceous lesion, with poorly defined limits, on the sole of the right foot.

Figure 2

Dermoscopy showed homogeneous global pattern of violaceous staining with blackened red dots, distributed inside the lesion.

Figure 3

Histopathology. Papillary projections with vascular axes lined by rounded and hyperchromatic cells – “Hobnail cells” (Hematoxylin & eosin, ×100).

Figure 4

Histopathology. Higher magnification with rounded and hyperchromatic cells that are protruding into the lumen – “hobnail cells” (Hematoxylin & eosin, ×400).