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Case Reports
. 2020 Mar;21(1):77-80.
doi: 10.30476/DENTJODS.2019.44910.

Melanotic Neuroectodermal Tumor of Infancy, a Rapidly Growing Maxillary Alveolar Mass: A Case Report

Saede Atarbashi-Moghadam  1 , Ali Lotfi  1 , Mohammad Moshref  1 , Fazele Atarbashi-Moghadam  2
Affiliations
Case Reports

Melanotic Neuroectodermal Tumor of Infancy, a Rapidly Growing Maxillary Alveolar Mass: A Case Report

Saede Atarbashi-Moghadam et al. J Dent (Shiraz). 2020 Mar.

Abstract

Melanotic neuroectodermal tumor of infancy is a rare, rapidly growing, painless, pigmented neoplasm with neural crest derivation. It usually occurs during the first year of life and there is a prominent predilection for the maxilla. The purpose of the present report is to describe additional case of melanotic neuroectodermal tumor of infancy of maxilla in a 6-month-old infant male. The treatment included surgical excision with safe margins. No attempt was made for immediate grafting of the surgery site due to high proliferation rate of tissues and self-renewal during infancy. The facial growth was normal and the surgical cleft was tightly closed. Due to the rarity of tumor, essential knowledge on characteristics of this lesion would contribute to a proper diagnosis and benefit treatment planning.

Keywords: Infant; Neuroectodermal Tumor, Melanotic; Pigmentation; Soft tissue neoplasm.

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Figures

Figure1
Figure1
A firm, projecting mass on left maxillary anterior alveolar ridge in a 6-month-old boy
Figure2
Figure2
The gross specimen shows a circumscribed mass with black cut surface.
Figure3
Figure3
a: Section shows a biphasic population of cells that form nests consisting of large epithelioid cells and small rounded neuroblast-like cells ×100. b: Large epithelioid cells containing melanin pigmentation (red arrows) and small rounded neuroblast-like cells (orange arrows) ×400
See this image and copyright information in PMC

References

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