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Case Reports
. 2020 Mar 3:26:e00185.
doi: 10.1016/j.crwh.2020.e00185. eCollection 2020 Apr.

Right-sided obstructed hemivagina ipsilateral renal agenesis (OHVIRA): A case report

Vaishnavi Malarazhagan  1 , Mayooran Veerasingham  1 , Kanapathippillai Sivanesan  1
Affiliations
Case Reports

Right-sided obstructed hemivagina ipsilateral renal agenesis (OHVIRA): A case report

Vaishnavi Malarazhagan et al. Case Rep Womens Health. .

Abstract

Introduction: Obstructed hemivagina ipsilateral renal agenesis (OHVIRA) is a rare anomaly of the urogenital system. The characteristic triad of this syndrome, which was initially reported in 1950, is didelphys uterus, obstructed hemivagina, and ipsilateral renal agenesis (Embrey, 1950 [1]).

Case: A 17-year-old girl was referred with a 6-month history of offensive vaginal discharge. Magnetic resonance imaging (MRI) established the diagnosis of OHVIRA. She underwent surgery for drainage of the hematocolpos and excision of the vaginal septum followed by an uncomplicated recovery and the patient had normal menstrual cycles after surgery.

Conclusion: There should be a high suspicion of OHVIRA syndrome when encountering adolescent patients with non-specific abdominal or pelvic symptoms.

Keywords: Didelphys and bicollis; MRI, magnetic resonance imaging; Mullerian anomaly; OHVIRA; OHVIRA, Obstructed hemivagina ipsilateral renal agenesis; Obstructed hemivagina; Renal agenesis; USS, ultrasound scan; Urogenital malformation.

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Figures

Fig. 1
Fig. 1
MRI coronal view demonstrating left (L) and right (R) uterine horns with left and right vagina.
Fig. 2
Fig. 2
MRI transverse view demonstrating right obstructed hemivagina (R) with vaginal septum (S) and left vagina (L).
Fig. 3
Fig. 3
Retractor (R) against vaginal septum (S) and left cervix (C) exposed. (For interpretation of the references to color in this figure, the reader is referred to the web version of this article.)
Fig. 4
Fig. 4
After excision of septum with dilator in both cervix. (For interpretation of the references to color in this figure, the reader is referred to the web version of this article.)
Fig. 5
Fig. 5
After entire septum excised and raw edges sutured. (For interpretation of the references to color in this figure, the reader is referred to the web version of this article.)
See this image and copyright information in PMC

References

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