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. 2020 Mar-Apr;23(2):159-166.
doi: 10.4103/aian.AIAN_190_19. Epub 2020 Feb 25.

Idiopathic Intracranial Hypertension: The Monster Within

Aastha Takkar  1 , Vivek Lal  1
Affiliations

Idiopathic Intracranial Hypertension: The Monster Within

Aastha Takkar et al. Ann Indian Acad Neurol. 2020 Mar-Apr.

Abstract

Idiopathic intracranial hypertension (IIH) is defined as a syndrome of raised intracranial pressure with normal imaging of the brain and cerebrospinal fluid (CSF) composition. There are many controversies and myths that surround IIH. Although patients of IIH may present "typical" symptoms and signs of raised intracranial pressure, clinical scenarios often vary. A typical clinical and radiological finding poses significant problems in diagnosis and management of patients with IIH. We have tried to resolve these controversies and provide a comprehensive update on different aspects of IIH. In this article, we review the common problems encountered while dealing with patients of IIH.

Keywords: Benign intracranial hypertension; headache; idiopathic intracranial hypertension; pseudotumor cerebri syndrome; visual loss.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Showing bilateral papilledema (a, b) on fundus examination; Normal visual field of the right eye (c) and constriction of field and enlarged blind spot of the left eye (d). MRI Brain showing Tortuous optic nerves (e) and Normal MR Venography (f)
Figure 2
Figure 2
Showing- a: Grade 1 papilledema; b: Grade 2 papilledema, c: Grade 3 papilledema; d: Grade 4 papilledema and e: Grade 5 papilledema
Figure 3
Figure 3
Showing MRI findings in IIH. (a) Showing Distension of Optic Nerve Sheath (T2 Weighted; axial view); (b) Showing Distension of Optic Nerve Sheath (T2 Weighted; coronal view); (c) Showing Tortuosity of Optic Nerve (Blue Arrow) and Scleral Indentation (Green Arrow)
See this image and copyright information in PMC

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