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Case Reports
. 2019 Jun 6;32(2):216-218.
doi: 10.4103/tcmj.tcmj_13_19. eCollection 2020 Apr-Jun.

An interesting case of Herlyn-Werner-Wunderlich syndrome

Maureen P Tigga  1
Affiliations
Case Reports

An interesting case of Herlyn-Werner-Wunderlich syndrome

Maureen P Tigga. Tzu Chi Med J. .

Abstract

Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare congenital anomaly characterized by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. Usually, such patients present with dysmenorrhea shortly after menarche, increasing pelvic pain and a palpable mass due to the obstructed hemivagina. Interestingly in the present case, the patient had her menarche seven years ago, but dysmenorrhea started only 1-year back. She never sought medical help previously as she was mostly asymptomatic all through the years. It was only after she conceived and got investigated for antenatal concerns that she was found to have HWWS. A tortuous history and an unusual clinical presentation made this case an interesting one.

Keywords: Herlyn–Werner–Wunderlich syndrome; Mullerian duct anomaly; Pandora's box.

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Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Intravenous pyelogram showing absent right kidney
Figure 2
Figure 2
Magnetic resonance imaging showing didelphic uterus with a huge cystic abdominal lump and absent right kidney
Figure 3
Figure 3
On laparotomy huge right-sided mucinous cystadenoma seen with normal right fallopian tube
Figure 4
Figure 4
Postcystadenectomy the didelphic uterus is uncovered. The two uterine horns are seen with normal fallopian tubes, normal left ovary and the right ovarian stump. No evidence of endometriosis seen elsewhere
See this image and copyright information in PMC

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