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Case Reports
. 2020 May 6;8(9):1745-1751.
doi: 10.12998/wjcc.v8.i9.1745.

Portal hypertension in a patient with biliary hamartomas: A case report

Qian-Qian Li  1 , Xiao-Zhong Guo  1 , Hong-Yu Li  1 , Xing-Shun Qi  2
Affiliations
Case Reports

Portal hypertension in a patient with biliary hamartomas: A case report

Qian-Qian Li et al. World J Clin Cases. .

Abstract

Background: Biliary hamartomas (BH) are a rare benign disease caused by malformation of the intrahepatic bile ducts. BH are occasionally diagnosed, but often lack obvious clinical symptoms. They are usually diagnosed by biopsy and imaging tests in clinical practice. Few studies have reported the association of BH with portal hypertension.

Case summary: A 40-year-old man was repeatedly admitted to our hospital due to hematochezia. The source of bleeding was considered to be gastroesophageal varices and portal hypertensive gastropathy by endoscopy. He had no history of hepatitis virus infection, alcohol abuse, drug-induced liver injury, or autoimmune liver disease. He underwent magnetic resonance imaging, which showed rounded, irregular, low-signal-T1 and high-signal-T2 lesions diffusely distributed on the liver, that were not communicated with the biliary system on magnetic resonance cholangiopancreatography. According to the imaging examination, the patient was considered to have a diagnosis of BH with portal hypertension.

Conclusion: Based on the present case report, BH may be a potential etiology of portal hypertension.

Keywords: Biliary hamartomas; Case report; Computed tomography; Magnetic resonance imaging; Portal hypertension; Variceal bleeding.

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Conflict of interest statement

Conflict-of-interest statement: The authors declare that they have no conflict of interest.

Figures

Figure 1
Figure 1
Computed tomography images of biliary hamartomas on September 21, 2018. A, B: Un-enhanced phases; C, D: Arterial phases; E, F: Portal vein phases.
Figure 2
Figure 2
Magnetic resonance imaging images of biliary hamartomas on September 25, 2018. A, B: T1-weighted; C, D: T2-weighted.
Figure 3
Figure 3
Magnetic resonance cholangiopancreatography image of biliary hamartomas on September 25, 2018.
Figure 4
Figure 4
Magnetic resonance imaging images of biliary hamartomas on July 7, 2019. A, B: T1-weighted; C, D: T2-weighted.
Figure 5
Figure 5
Magnetic resonance cholangiopancreatography image of biliary hamartomas on July 7, 2019.
See this image and copyright information in PMC

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